A New Insight over Telangiectasia Macularis Eruptiva Perstans

  • André Pinho Interno complementar de Dermatologia e Venereologia/Residente, Dermatology and Venereology, Serviço de Dermatologia, Centro Hospitalar e Universitário de Coimbra, Coimbra, Portugal
  • José Carlos Cardoso Assistente Hospitalar/Consultant of Dermatology and Venereology, Serviço de Dermatologia, Centro Hospitalar e Universitário de Coimbra, Coimbra, Portugal
  • Hugo Oliveira Assistente Hospitalar/Consultant of Dermatology and Venereology, Serviço de Dermatologia, Centro Hospitalar e Universitário de Coimbra, Coimbra, Portugal
  • Óscar Tellechea Chefe de Serviço/Consultant Chief of Dermatology and Venereology, Serviço de Dermatologia, Centro Hospitalar e Universitário de Coimbra, Coimbra, Portugal
  • Américo Figueiredo Professor e Director do Serviço de Dermatologia/Professor and Head of Dermatology Department, Centro Hospitalar e Universitário de Coimbra, Portugal
Keywords: Mastocytosis, Cutaneous, Telangiectasis, Urticaria Pigmentosa

Abstract

Telangiectasia macularis eruptiva perstans (TMEP) is a rare form of cutaneous mastocytosis with distinctive semiology and histopathology, but that is not free of controversy regarding its individualization as a nosological entity. For some authors, the presence of exclusively telangiectatic macules, along with superficial vascular plexus dilation and low density of mast cell infiltrates in the upper dermis is enough for diagnosis of TMEP. However, some current classifications do not consider this entity separately from other types of cutaneous mastocytosis, because in many cases with telangiectatic lesions, lesions of urticaria pigmentosa can also be observed. We sought to present a case of cutaneous mastocytosis first appearing in the eighth decade of life, with the characteristic clinical, dermoscopic and histopathological findings of TMEP and with no mast cell activation symptoms other than pruritus. However, the complementary workup revealed concurrently the presence of indolent systemic mastocytosis. We additionally revised the most recent evidence favouring the recognition and individualization of this entity.

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Published
2016-10-15
How to Cite
Pinho, A., Cardoso, J. C., Oliveira, H., Tellechea, Óscar, & Figueiredo, A. (2016). A New Insight over Telangiectasia Macularis Eruptiva Perstans. Journal of the Portuguese Society of Dermatology and Venereology, 74(3), 291-297. https://doi.org/10.29021/spdv.74.3.601
Section
Case Reports