Um Caso Clínico de Lepra Multibacilar com Vários Surtos de Eritema Nodoso Leproso

R. Bouceiro-Mendes, A. Ortins-Pina, T. Marques, M. Viveiros, D. Machado, L. Lito, J. Ferreira, L. Soares-de-Almeida, J. P. Freitas, P. Filipe

Resumo


A lepra é uma doença granulomatosa crónica com longo período de incubação causada pelo bacilo Mycobacte- -rium leprae que afeta principalmente a pele, mucosas e sistema nervoso periférico. Tem risco de sequelas permanentes e impacto significativo na qualidade de vida do paciente. É clinicamente heterogénea com possíveis apresentações atípicas. Descrevemos o caso de uma mulher de 31 anos, fototipo V, com lepra multibacilar caracterizada por múltiplos surtos de eritema nodoso leproso como manifestação inaugural. A doença foi adquirida num grupo de crianças e adolescentes de uma região endémica de África, evoluiu sem tratamento durante 3 anos, e manifestou-se com algumas características clínicas incomuns e notável envolvimento linfático. Destacamos a importância da colaboração entre centros especializados e parcerias institucionais, a fim de fornecer os recursos de diagnósti-co e os cuidados adequados às populações afetadas.


Palavras-chave


Eritema Nodoso; Lepra Lepromatosa; Lepra Multibacilar

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Referências


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DOI: http://dx.doi.org/10.29021/spdv.77.1.1015

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