A Case Report of Multibacillary Leprosy Presenting with Multiple Outbreaks of Erythema Nodosum Leprosum

R. Bouceiro-Mendes, A. Ortins-Pina, T. Marques, M. Viveiros, D. Machado, L. Lito, J. Ferreira, L. Soares-de-Almeida, J. P. Freitas, P. Filipe

Abstract


Leprosy is a chronic granulomatous disease with a long incubation period caused by Mycobacterium leprae that mainly affects the skin, mucous membranes and the peripheral nervous system. It carries the risk of per-manent sequels with a significant impact on the patient’s quality of life. It has a considerable clinically diver-sity and possible atypical presentations. We present a case of a 31-year-old, skin phototype V woman with multibacillary leprosy characterized by multiple outbreaks of erythema nodosum leprosum, as an inaugural manifestation of the disease. The disease was acquired within a group of children and adolescents from an endemic region of Africa, evolved untreated for 3 years, and presented with unusual features and remarkable lymphatic involvement. We highlight the importance of building and maintaining collaboration between expert centers and institutional partnerships in order to provide the adequate diagnostic resources and appropriate care to the affected populations.


Keywords


Erythema Nodosum; Leprosy, Lepromatous; Leprosy, Multibacillary

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References


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DOI: http://dx.doi.org/10.29021/spdv.77.1.1015

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