Juvenile scleroderma is a disease that has different features in comparison to scleroderma in adults. Its incidence is rare on infancy. It can be systemic or localized and, this last form is more frequent. We report a case of juvenile scleroderma in a 3-year-old female child presenting with a yellow plaque on the trunk simulating a xantomathous lesion. The lilac ring around the lesion contributed to the construction of the correct diagnostic hypothesis which was confirmed by the histopathology. The precocious diagnosis on this case, allowed the beginning of the treatment on an initial phase of the disease, contributing to a better prognosis for the patient.
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