Pustular Eruptions in Children as Manifestations of Autoinflammatory Diseases

  • Felicidade Santiago Assistente Hospitalar de Dermatologia e Venereologia/Consultant of Dermatology and Venereology, Centro Hospitalar de Leiria, Portugal http://orcid.org/0000-0003-2402-4229
  • Antonio Torrelo Assistente Hospitalar de Dermatologia e Venereologia/Consultant of Dermatology and Venereology, Hospital Infantil Universitario Niño Jesús, Madrid, Spain https://orcid.org/0000-0002-5940-6916
Keywords: Child, Hereditary Autoinflammatory Diseases/complications, Skin Diseases/etiology, Skin Diseases, Vesiculobullous/ etiology

Abstract

Nowadays, in clinical practice, when attending a child with a pustular eruption and systemic inflammation, it is mandatory to think of an autoinflammatory disease, once infectious causes have been ruled out. Although rare, autoinflammatory disease must be recognized as early as possible, accurately diagnosed (including gene testing), and treated with targeted therapy if available.

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Published
2019-07-12
How to Cite
Santiago, F., & Torrelo, A. (2019). Pustular Eruptions in Children as Manifestations of Autoinflammatory Diseases. Journal of the Portuguese Society of Dermatology and Venereology, 77(2), 145-152. https://doi.org/10.29021/spdv.77.2.1066
Section
Review Articles