Pustular Eruptions in Children as Manifestations of Autoinflammatory Diseases

Felicidade Santiago; Antonio Torrelo

doi:10.29021/spdv.77.2.1066

Felicidade Santiago Assistente Hospitalar de Dermatologia e Venereologia/Consultant of Dermatology and Venereology, Centro Hospitalar de Leiria, Portugal http://orcid.org/0000-0003-2402-4229
Antonio Torrelo Assistente Hospitalar de Dermatologia e Venereologia/Consultant of Dermatology and Venereology, Hospital Infantil Universitario Niño Jesús, Madrid, Spain https://orcid.org/0000-0002-5940-6916

DOI: https://doi.org/10.29021/spdv.77.2.1066

Keywords: Child, Hereditary Autoinflammatory Diseases/complications, Skin Diseases/etiology, Skin Diseases, Vesiculobullous/ etiology

Abstract

Nowadays, in clinical practice, when attending a child with a pustular eruption and systemic inflammation, it is mandatory to think of an autoinflammatory disease, once infectious causes have been ruled out. Although rare, autoinflammatory disease must be recognized as early as possible, accurately diagnosed (including gene testing), and treated with targeted therapy if available.

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