Erupções Pustulosas em Crianças como Manifestações de Doenças Auto-Inflamatórias

Palavras-chave: Criança, Dermatopatias Vesiculobolhosas/etiologia, Doenças da Pele/etiologia, Doenças Hereditárias Autoinflamatórias/complicações

Resumo

Atualmente, na prática clínica, quando se observa uma criança com uma erupção pustulosa e inflamação sistémica, é mandatório pensar numa doença auto-inflamatória, após excluir uma causa infecciosa. Apesar de rara, a doença auto- -inflamatória deve ser reconhecida o mais precocemente possível, diagnosticada corretamente (incluindo estudo genético), e tratada com terapia dirigida, se disponível.

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Publicado
2019-07-12
Como Citar
Santiago, F., & Torrelo, A. (2019). Erupções Pustulosas em Crianças como Manifestações de Doenças Auto-Inflamatórias. Revista Da Sociedade Portuguesa De Dermatologia E Venereologia, 77(2), 145-152. https://doi.org/10.29021/spdv.77.2.1066
Secção
Artigo de Revisão