LANGERHANS CELL HISTIOCYTOSIS

  • Fátima Satomi Nishimori Residente do terceiro ano de Dermatologia/Resident of the third year of Dermatology, Hospital Federal da Lagoa, Rio de Janeiro, Brasil
  • Gabriel Monteiro de Castro Chaves Residente do primeiro ano de Dermatologia/Resident of the first year of Dermatology, Instituto de Dermatologia Professor Rubem David Azulay, Rio de Janeiro, Brasil
  • Camila Nemoto de Mendonça Residente do terceiro ano de Dermatologia/Resident of the third year of Dermatology, Hospital Federal da Lagoa, Rio de Janeiro, Brasil
  • Priscila Mara Chaves e Silva Residente do segundo ano de Dermatologia/Resident of the second year of Dermatology, Hospital Federal da Lagoa, Rio de Janeiro, Brasil
  • Calisqui Bradenburg Fernandes Residente do primeiro ano de Endocrinologia/Resident of the first year of Endocrinology, Hospital Federal da Lagoa, Rio de Janeiro, Brasil
  • Leonardo Vieira Neto Professor do Departamento de Clínica Médica e Serviço de Endocrinologia – Faculdade de Medicina e Hospital Universitário Clementino Fraga filho – Universidade Federal do Rio de Janeiro, Brasil/Professor of the Department of Internal Medicine and Endocrine Unit – Medical School and Clementino Fraga Filho University Hospital – Federal University of Rio de Janeiro. Endocrinologista do Serviço de Endocrinologia do Hospital Federal da Lagoa/ Endocrinologist of Endocrine Unit – Hospital Federal da Lagoa, Rio de Janeiro, Brasil
  • João Carlos Regazzi Avelleira Especialista em Dermatologia pela Sociedade Brasileira de Dermatologia/Specialist in Dermatology; Chefe do Serviço de Dermatologia/Head of the Dermatology Department, Hospital Federal da Lagoa, Rio de Janeiro, Brasil
DOI: https://doi.org/10.29021/spdv.72.2.260
Keywords: Histiocytosis, Langerhans cell

Abstract

The authors report a case of a young male patient who presented with erythematous and descamative lesions, with maceration, in the axillary and inguinal region, associated with erythematous ulcerated plaques in the perianal region. Histopathological examination was compatible with Langerhans cell histiocytosis, with immunohistochemical positivity for CD1a and S100, thus confirming the diagnosis. Systemic investigation revealed an extra-axial mass in supra-sellar region; he underwent chemotherapy, with a significant improvement of the cutaneous lesions. He keeps his follow-up by the Dermatology, Hematology and Endocrinology Units.

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Published
2014-09-19
How to Cite
Nishimori, F. S., Chaves, G. M. de C., de Mendonça, C. N., Chaves e Silva, P. M., Fernandes, C. B., Neto, L. V., & Avelleira, J. C. R. (2014). LANGERHANS CELL HISTIOCYTOSIS. Journal of the Portuguese Society of Dermatology and Venereology, 72(2), 227-231. https://doi.org/10.29021/spdv.72.2.260
Issue
Vol 72 No 2 (2014): Abril - Junho
Section
Case Reports

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