ATYPICAL FIBROXANTHOMA – RARE TUMOR ARISING IN A BURN SCAR

  • Ana Gameiro Médico Interno do Internato Médico de Dermatovenereologia/Resident, Dermatology, Serviço de Dermatologia, Centro Hospitalar e Universitário de Coimbra, Coimbra, Portugal
  • Miguel Gouveia Médico Interno do Internato Médico de Dermatovenereologia/Resident, Dermatology, Serviço de Dermatologia, Centro Hospitalar e Universitário de Coimbra, Coimbra, Portugal
  • Ana Brinca Assistente Hospitalar de Dermatovenereologia/Consultant, Dermatology, Serviço de Dermatologia, Centro Hospitalar e Universitário de Coimbra, Coimbra, Portugal
  • José Carlos Cardoso Assistente Hospitalar de Dermatovenereologia/Consultant, Dermatology, Serviço de Dermatologia, Centro Hospitalar e Universitário de Coimbra, Coimbra, Portugal
  • Ricardo Vieira Assistente Hospitalar de Dermatovenereologia/Consultant, Dermatology, Serviço de Dermatologia, Centro Hospitalar e Universitário de Coimbra, Coimbra, Portugal; Professor Auxiliar da Faculdade de Medicina/Associated Professor, Universidade de Coimbra, Portugal
Keywords: Atypical Fibroxanthoma, Undifferentiated Pleomorphic Sarcoma, Skin Tumors, Scar, Burn

Abstract

Atypical fibroxanthoma (AFX) is a relatively rare cutaneous tumor, characteristically presenting as a rapidly growing solitary nodule in photo-exposed areas of elderly patients. In spite of worrisome histological features, like pleomorphism and high mitotic rate, prognosis is favorable. Case report: A 62-year-old woman, with cicatricial alopecia on the parietal area, secondary to a thermal burn in her childhood, presented an ulcero-vegetant tumor, on the alopecia area, evolving for 1 year. Histology and immunohistochemistry showed features suggestive of AF. The tumor was completely excised, and a double transposition flap was used for closure, achieving local tumor control. The risk factors for AFX are not completely defined. Nevertheless, chronic exposition to ultraviolet radiation is a primordial factor. Other risk factors are radiotherapy and immunosuppression. Burn scars were only sporadically described in association to AF.

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Published
2016-01-28
How to Cite
Gameiro, A., Gouveia, M., Brinca, A., Cardoso, J. C., & Vieira, R. (2016). ATYPICAL FIBROXANTHOMA – RARE TUMOR ARISING IN A BURN SCAR. Journal of the Portuguese Society of Dermatology and Venereology, 73(4), 497-500. https://doi.org/10.29021/spdv.73.4.494
Section
Case Reports