ATYPICAL FIBROXANTHOMA – RARE TUMOR ARISING IN A BURN SCAR
Abstract
Atypical fibroxanthoma (AFX) is a relatively rare cutaneous tumor, characteristically presenting as a rapidly growing solitary nodule in photo-exposed areas of elderly patients. In spite of worrisome histological features, like pleomorphism and high mitotic rate, prognosis is favorable. Case report: A 62-year-old woman, with cicatricial alopecia on the parietal area, secondary to a thermal burn in her childhood, presented an ulcero-vegetant tumor, on the alopecia area, evolving for 1 year. Histology and immunohistochemistry showed features suggestive of AF. The tumor was completely excised, and a double transposition flap was used for closure, achieving local tumor control. The risk factors for AFX are not completely defined. Nevertheless, chronic exposition to ultraviolet radiation is a primordial factor. Other risk factors are radiotherapy and immunosuppression. Burn scars were only sporadically described in association to AF.
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References
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