Pseudoainhum in a Patient with Mixed Connective Tissue Disease: An Uncommon Association

  • Sara Campos Resident of Dermatovenereology, Dermatovenereology Department, Hospital Santo António dos Capuchos - Centro Hospitalar Lisboa Central, Lisbon, Portugal
  • Ana Brasileiro Consultant of Dermatovenereology, Dermatovenereology Department, Hospital Santo António dos Capuchos - Centro Hospitalar Lisboa Central, Lisbon, Portugal
  • Joana Cabete Consultant of Dermatovenereology, Dermatovenereology Department, Hospital Santo António dos Capuchos - Centro Hospitalar Lisboa Central, Lisbon, Portugal
  • Sofia Pinheiro Consultant of Internal Medicine, Internal Medicine Department, Hospital Santo António dos Capuchos - Centro Hospitalar Lisboa Central, Lisbon, Portugal
  • André Lencastre Consultant of Dermatovenereology, Dermatovenereology Department, Hospital Santo António dos Capuchos - Centro Hospitalar Lisboa Central, Lisbon, Portugal
  • Maria João Paiva Lopes Consultant of Dermatovenereology, Dermatovenereology Department, Hospital Santo António dos Capuchos - Centro Hospitalar Lisboa Central, Lisbon, Portugal
Keywords: Ainhum/complications, Constriction, Pathologic, Mixed Connective Tissue Disease

Abstract

The term pseudoainhum is used to describe constricting band(s) around one or more digits in relation to several congenital or acquired diseases. Systemic sclerosis, keratoderma, psoriasis, Reynolds syndrome among others, has been reported to be associated with pseudoainhum development. We report a case of a 54 years old woman with annular constricting bands and micronychia on the fourth and fifth digits of her both hands associated with bilateral distal acrosclerosis. Raynaud’s phenomenon with some years of evolution and, more recent, fatigue and recurrent inflammatory polyarthritis and also antinuclear and anti-U1 nuclear ribonucleoprotein antibodies were present. Therefore, the diagnoses of pseudoainhum with a likely association with mixed connective tissue disease were proposed. Whenever in the presence of pseudoainhum, a detailed workup, including autoimmune disorders screening, is mandatory in order to rule out possible associated syndromes or underlying diseases. The authors present this case as the association between pseudoainhum and mixed connective tissue disease has not been previously reported in the literature.

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Published
2017-04-17
How to Cite
Campos, S., Brasileiro, A., Cabete, J., Pinheiro, S., Lencastre, A., & Paiva Lopes, M. J. (2017). Pseudoainhum in a Patient with Mixed Connective Tissue Disease: An Uncommon Association. Journal of the Portuguese Society of Dermatology and Venereology, 75(1), 83-85. https://doi.org/10.29021/spdv.75.1.723
Section
Case Reports