Cutaneous Disseminated Juvenile Xanthogranuloma: A Case Report

Débora Bacellar Cruz Nunes, Adriana Kamilly Leitão Pitman Machado, Michele Fonseca Goiabeira, Yandra Sherring Einecke, Alena Bacellar Cruz Nunes, Maria Amélia Lopes dos Santos, Francisca Regina Oliveira Carneiro


Juvenile xanthogranuloma (JXG) is a benign self-limiting histiocytosis, currently classified as a disorder derived from dendrocytes and previously classified as non-Langerhans cell histiocytosis. It usually manifests as a solitary and asymptomatic lesion occurring most often in patients younger than one year of age and most cases resolve completely in three to six years, but systemic involvement may occur. The authors report a case of juvenile xanthogranuloma with an uncommon clinical presentation with disseminated lesions confirmed by the dermatoscopic, histopathologic, and immunohistochemical patterns that allowed the exclusion of possible differential diagnosis.


Dermoscopy; Xanthogranuloma, Juvenile/diagnosis; Xanthogranuloma, Juvenile/pathology

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