Extracutaneous Manifestations of Localized Scleroderma: A Review

  • F. Morgado Serviço de Dermatologia, Centro Hospitalar e Universitário de Coimbra, Coimbra, Portugal
  • M. Batista Serviço de Dermatologia, Centro Hospitalar e Universitário de Coimbra, Coimbra, Portugal
  • H. Oliveira Serviço de Dermatologia, Centro Hospitalar e Universitário de Coimbra, Coimbra, Portugal
  • M. Gonçalo Serviço de Dermatologia, Centro Hospitalar e Universitário de Coimbra, Coimbra, Portugal
Keywords: Scleroderma, Localized/classification, Localized/complications, Localized/physiopathology

Abstract

Morphea or localized scleroderma is a connective tissue disorder in which excess collagen deposition leads to the development of sclerotic lesions. Initially distinguished from systemic sclerosis by the absence of systemic manifestations, involvement limited to the skin and a relatively benign course, it is now known that localized sclerosis may be associated with multiple extracutaneous manifestations. This article reviews the musculoskeletal, neurological, ophthalmological, gastrointestinal, respiratory, cardiac and renal manifestations of this disease.

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Author Biography

F. Morgado, Serviço de Dermatologia, Centro Hospitalar e Universitário de Coimbra, Coimbra, Portugal
Serviço de Dermatologia - Centro Hospitalar e Universitário de Coimbra

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Published
2018-05-29
How to Cite
Morgado, F., Batista, M., Oliveira, H., & Gonçalo, M. (2018). Extracutaneous Manifestations of Localized Scleroderma: A Review. Journal of the Portuguese Society of Dermatology and Venereology, 76(2), 127-136. https://doi.org/10.29021/spdv.76.2.881
Section
Continuous Medica Education