Multiple Adult Xanthogranuloma: Case Report and Brief Literature Review

  • Felipe Siqueira Ramos Médico Especializando do 1º ano de Dermatologia do Hospital Universitário de Taubaté - HUT/UNITAU – Taubaté-SP, Brasil
  • Flávia Regina Ferreira Mestre e Doutora em Ciências pela Universidade Federal de São Paulo -UNIFESP/EPM - Professora Assistente III da disciplina de Dermatologia do Departamento de Medicina da Universidade de Taubaté / Médica do Serviço de Dermatologia do Hospital Universitário de Taubaté - HUT/UNITAU – Taubaté-SP, Brasil
  • Samuel Henrique Mandelbaum Especialista em Dermatologia - Professor Assistente da disciplina de Dermatologia do Departamento de Medicina da Universidade de Taubaté/ Chefe do Serviço de Dermatologia do Hospital Universitário de Taubaté - HUT/ UNITAU – Taubaté-SP, Brasil
  • Fernanda da Rocha Gonçalves Especialista em Patologia - Médica Patologista Assistente do Hospital do Servidor Público Estadual – São Paulo-SP, Brasil
DOI: https://doi.org/10.29021/spdv.76.2.950
Keywords: Adult, Granuloma, Histiocytosis, Non-Langerhans-Cell, Skin Diseases, Xanthomatosis

Abstract

Multiple adult xanthogranuloma is a non-Langerhans cell histiocytosis, a rare variant of the juvenile xanthogranuloma. The etiology is unknown, affecting individuals predominantly below 30 years of age, without predilection for gender. Clinically presents itself as multiple, disseminated, yellow-brownish papules or nodules. Diagnostic confirmation is given by histopathology and by immunohistochemistry, which further allow to distinguish it from Langerhans cell histiocytosis. The spontaneous regression is uncommon. We report a classic, rare and clinically exuberant case of multiple adult xanthogranuloma and took the opportunity to perform a brief literature review on the topic.

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References

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Published
2018-05-29
How to Cite
Siqueira Ramos, F., Ferreira, F. R., Mandelbaum, S. H., & da Rocha Gonçalves, F. (2018). Multiple Adult Xanthogranuloma: Case Report and Brief Literature Review. Journal of the Portuguese Society of Dermatology and Venereology, 76(2), 193-196. https://doi.org/10.29021/spdv.76.2.950
Issue
Vol 76 No 2 (2018): April - June
Section
Case Reports

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