Linfoma Cutâneo Primário de Grandes Células B, Tipo Perna: Relato de Caso com Apresentação Rara

N. A.  Sousa; M. O. Buffara; R. L. Maia; A. S. Pessoa; FF Cassia; A. M. Brotas

doi:10.29021/spdv.78.1.1144

N. A. Sousa Departamento de Dermatologia, Hospital Universitário Pedro Ernesto, Rio de Janeiro, Brasil https://orcid.org/0000-0002-3619-2011
M. O. Buffara Departamento de Dermatologia, Hospital Universitário Pedro Ernesto, Rio de Janeiro, Brasil https://orcid.org/0000-0002-1583-0125
R. L. Maia Departamento de Dermatologia, Hospital Universitário Pedro Ernesto, Rio de Janeiro, Brasil https://orcid.org/0000-0001-5214-1022
A. S. Pessoa Departamento de Dermatologia, Hospital Universitário Pedro Ernesto, Rio de Janeiro, Brasil https://orcid.org/0000-0002-0608-8918
FF Cassia Doutora em Dermatologia pela Universidade Federal do Rio de Janeiro, Rio de Janeiro, Brasil https://orcid.org/0000-0001-6944-3000
A. M. Brotas Departamento de Dermatologia, Hospital Universitário Pedro Ernesto, Rio de Janeiro, Brasil https://orcid.org/0000-0001-9830-4763

DOI: https://doi.org/10.29021/spdv.78.1.1144

Palavras-chave: Linfoma Difuso de Grandes Células B/diagnóstico, Linfoma Difuso de Grandes Células B/tratamento, Neoplasias da Pele

Resumo

Linfomas cutâneos primários são definidos como um grupo heterogéneo de neoplasias malignas linfoproliferativas que acometem a pele, sem evidência de envolvimento extracutâneo no momento do diagnóstico. O subgrupo “linfoma cutâneo primário de grandes células B, tipo perna (PCLBCL, LT)” geralmente acomete um ou ambos membros inferiores, porém 10% - 15% dos casos apresentam lesões em outros locais. Apresenta-se um caso raro de PCLBCL, LT com lesão nodular na região cervical posterior, enfatizando sua apresentação atípica. Considerando o crescimento rápido da lesão e o alto índice proliferativo, é importante conhecer todas as possíveis apresentações clínicas para assim realizar o diagnóstico precoce e instituir o tratamento efetivo.

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