Primary Cutaneous Diffuse Large B Cell Lymphoma Leg Type. An Atypical Presentation

Keywords: Lymphoma, Large B-Cell, Diffuse/diagnosis, Lymphoma, Large B-Cell, Diffuse/therapy, Skin Neoplasms

Abstract

Primary cutaneous lymphomas are defined as a heterogeneous group of malignant lymphoproliferative neoplasms that attack the skin, without extracutaneous involvement at the moment of the diagnosis. The subgroup "primary cutaneous lymphoma of great cells B, leg type (PCLBCL, LT)" generally attacks one or both lower limbs, however in 10% - 15 % of the cases other areas of the skin may be affected. We present a rare case of PCLBCL, LT with a nodular lesion located in the cervical region to empathize an atypical presentation. Considering its quick growth and high proliferative rate, it is of great importance to know all its possible clinical presentations for a precocious diagnosis and efficient treatment.

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Published
2020-05-06
How to Cite
Sousa, N. A., Buffara, M. O., Maia, R. L., Pessoa, A. S., Cassia, F., & Brotas, A. M. (2020). Primary Cutaneous Diffuse Large B Cell Lymphoma Leg Type. An Atypical Presentation. Journal of the Portuguese Society of Dermatology and Venereology, 78(1), 61-65. https://doi.org/10.29021/spdv.78.1.1144
Section
Case Reports