Congenital Syringocystadenoma Papilliferum

  • Yandra Sherring Einecke Serviço de Dermatologia da Universidade do Estado do Pará, Belém-PA, Brasil
  • Erica Baptista Pinto Serviço de Dermatologia da Universidade do Estado do Pará, Belém-PA, Brasil
  • Samira Oliveira Silveira Serviço de Dermatologia da Universidade do Estado do Pará, Belém-PA, Brasil
  • Maria Amélia Lopes dos Santos Serviço de Dermatologia da Universidade do Estado do Pará, Belém-PA, Brasil
  • Alena Margareth Darwich Mendes Serviço de Dermatologia da Universidade do Estado do Pará, Belém-PA, Brasil
  • Francisca Regina Oliveira Carneiro Serviço de Dermatologia da Universidade do Estado do Pará, Belém-PA, Brasil; Chefe do Serviço de Dermatologia da Universidade do Estado do Pará, Belém-PA, Brasil
DOI: https://doi.org/10.29021/spdv.76.1.743
Keywords: Adenoma, Sweat Gland/congenital, Cystadenoma, Skin Neoplasms, Syringoma

Abstract

Papillary syringocystoadenoma is an uncommon benign adnexal neoplasm, which is preferentially located on the scalp and face, and is associated with sebaceous nevus in 40% of cases. Although rare, its transition to basal cell carcinoma and ductal carcinoma may occur. The authors describe the case of a 7-year-old male patient with a linear papular dermatosis in the neck from birth. Dermatological examination showed erythematous, crateriform, confluent papules, arranged in a band, 3 x 2 cm in the cervical region. The lesion was excised for therapeutic and diagnostic purposes. Histopathology demonstrated epidermal cystic invagination and papillary projections surface by glandular epithelium, with decapitation secretion and abundant lymphoplasmocytic infiltrate. The clinical and histological findings were compatible with the diagnosis of papillary syringocystoadenoma. Despite the clinical variability of this entity, the histopathology is characteristic and the treatment consists in the excision of the lesion.

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Published
2018-04-05
How to Cite
Sherring Einecke, Y., Baptista Pinto, E., Oliveira Silveira, S., Lopes dos Santos, M. A., Darwich Mendes, A. M., & Oliveira Carneiro, F. R. (2018). Congenital Syringocystadenoma Papilliferum. Journal of the Portuguese Society of Dermatology and Venereology, 76(1), 79-82. https://doi.org/10.29021/spdv.76.1.743
Issue
Vol 76 No 1 (2018): Janeiro - Março
Section
Case Reports

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