Facial Sebaceous Nevus of Jadassohn: An Exuberant Presentation

  • Carolina Fernandes Pereira Médica Aperfeiçoanda do 2º ano de Dermatologia do Hospital Municipal Universitário de Taubaté, Taubaté, Brasil https://orcid.org/0000-0002-7567-6983
  • Mariana Patriota Naville Médica Aperfeiçoanda do 2º ano de Dermatologia do Hospital Municipal Universitário de Taubaté – H.MUT/UNITAU – Taubaté-SP, Brasil https://orcid.org/0000-0001-8666-1018
  • Flávia Regina Ferreira Mestre e Doutora em Ciências pela Universidade Federal de São Paulo - UNIFESP/EPM - Professora Assistente III da disciplina de Dermatologia do Departamento de Medicina da Universidade de Taubaté / Médica do Serviço de Dermatologia do Hospital Municipal Universitário de Taubaté – H.MUT/UNITAU – Taubaté-SP, Brasil https://orcid.org/0000-0001-5679-4282
  • Fernanda da Rocha Gonçalves Especialista em Patologia - Médica Patologista Assistente do Hospital do Servidor Público Estadual – São Paulo-SP, Brasil https://orcid.org/0000-0003-2933-2845
Keywords: Head and Neck Neoplasms, Infant, Nevus, Sebaceous of Jadassohn, Skin Neoplasms

Abstract

Sebaceous nevus of Jadassohn (SNJ) is an organoid hamartoma of the skin usually seen at or shortly after birth. Its most common location is the scalp, however, it may involve other areas of the head and neck. Classically it presents as a well- -defined plaque composed of multiple confluent yellowish-orange or yellow-brownish papules. The development of neoplasms in SNJ is well documented (10%-30%) as well as its possible association with a neurocutaneous syndrome. We report an exuberant case of facial SNJ in a 2-month-old male patient who underwent surgery at an early age. Recent literature on the subject is briefly addressed.

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Published
2020-05-06
How to Cite
Pereira, C. F., Patriota Naville, M., Regina Ferreira, F., & da Rocha Gonçalves, F. (2020). Facial Sebaceous Nevus of Jadassohn: An Exuberant Presentation. Journal of the Portuguese Society of Dermatology and Venereology, 78(1), 57-60. https://doi.org/10.29021/spdv.78.1.1136
Section
Case Reports

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